A male infant is failing to thrive and, on examination, is noted to have hepatomegaly and splenomegaly, among other findings. Urinalysis reveals the presence of both dermatan sulfate and heparan sulfate. You suspect the patient has Hurler syndrome. From the following list, select the enzyme

第1题

The Renaissance is characterized by admiration of the Greek and Latin.

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第2题

One of the disadvantages of participative budgeting is the slack.

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第3题

The Modigliani and Miller theory is based on perfect capital markets which do not exist in the real world.

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第4题

An increase in ROCE could be achieved by Increasing operating profit and capital employed.

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第5题

All of the following sugars are found in glycoproteins EXCEPT:

A、Fructose

B、Fucose

C、Galactose

D、Mannose

E、Xylose

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第6题

Select the one FALSE statement:

A、Mucins contain predominantly O-linked glycans.

B、O-linked sugar chains are built up by the stepwise donation of sugars from nucleotide-sugars.

C、Dolichol-pyrophosphate–oligosaccharide donates all of the sugars found in mature N-linked glycoproteins.

D、N-acetylneuraminic acid is commonly found at the termini of N-linked sugar chains.

E、Calnexin retains partly folded or misfolded proteins in the ER until proper folding has occurred.

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第7题

鞘糖脂的分子组成包括：

A、甘油

B、鞘氨醇

C、磷酸

D、糖链

E、脂肪酸

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第8题

体内重要的糖胺聚糖有：

A、硫酸软骨素

B、硫酸角质素

C、肝素

D、硫酸皮肤素

E、透明质酸

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第9题

以下说法正确的是：

A、糖蛋白和蛋白聚糖都是由糖与蛋白质两部分由共价键连接组成。

B、组成蛋白聚糖的糖链称为糖胺聚糖

C、组成糖蛋白的糖链可分为N-糖链和O-糖链

D、一般来说，糖蛋白分子中的蛋白质百分比小于糖，而蛋白聚糖则相反

E、组成糖蛋白和蛋白聚糖中的糖链结构迥然不同，功能也有差异

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